Anencephaly is birth defect of neural tube.The recurrent of anencephaly is a rare case. This study reports of a 35-years old woman gravida who detected her second fetal anencephaly in seventeenweeks gestation. She had her first fetal anencephaly seven years before which was late known in fourty weeks gestation. The awareness of high-risk maternal group of anencephaly is low. Management strategies should be promoted for preventing the recurrent case of anencephaly pregnancies.

Keywords : Anencephaly, Recurrent Anencephaly, Neural Tube Defect, Birth Defect, Rare Case