Authors :
Mirza Syafaryuni; Andi Alief Utama Armyn; Yulius Patimang; Muzakkir Amir; Idar Mappangara
Volume/Issue :
Volume 9 - 2024, Issue 4 - April
Google Scholar :
https://tinyurl.com/yeehr2f2
Scribd :
https://tinyurl.com/mrynbkwn
DOI :
https://doi.org/10.38124/ijisrt/IJISRT24APR2055
Abstract :
Background:
Twin pregnancies have a higher risk of congenital
heart defects compared to singleton pregnancies. The
most commonly found congenital heart defect in both
monochorionic and dichorionic twin gestations is
ventricular septal defect (VSD). Approximately 10% of
individuals with congenital heart defects will develop
pulmonary arterial hypertension-congenital heart disease
(PH-CHD).
Case Presentation:
We diagnosed an 11-year-old twin girl with
ventricular septal defect. First Patient had a severe PH
with mean Pulmonary Artery Pressure (mPAP) 68 and a
defect size of 9-12 mm, while second patient had a mild
PH with mPAP 30 and a defect size of 6-9 mm. The
patient presented with failure to thrive, exercise
intolerance during daily activities, and a history of
recurrent respiratory tract infections. Echocardiography
and right heart catheterization (RHC) results showed that
the first patient with VSD Left to Right Shunt with low
flow high resistance, non-reactive oxygen test and
pulmonary hypertension. The second patient with VSD
Let to Right shunt. Both of the patients were diagnosed
with ventricular septal defect (VSD) and pulmonary
hypertension (PH). However, they received different
treatments based on the RHC results.
Conclusion:
Promptly addressing the long-term implications of
CHD is essential to prevent pulmonary hypertension (PH)
and systemic disorders. Advanced PH treatments are safe
and can result in improved hemodynamic, exercise
capacity, quality of life, growth and development and
potentially survival.
Keywords :
Congenital Heart Disease, Ventricle Septal Disease, Twins, Pulmonary Arterial Hypertension, Right Heart Catheterization.
Background:
Twin pregnancies have a higher risk of congenital
heart defects compared to singleton pregnancies. The
most commonly found congenital heart defect in both
monochorionic and dichorionic twin gestations is
ventricular septal defect (VSD). Approximately 10% of
individuals with congenital heart defects will develop
pulmonary arterial hypertension-congenital heart disease
(PH-CHD).
Case Presentation:
We diagnosed an 11-year-old twin girl with
ventricular septal defect. First Patient had a severe PH
with mean Pulmonary Artery Pressure (mPAP) 68 and a
defect size of 9-12 mm, while second patient had a mild
PH with mPAP 30 and a defect size of 6-9 mm. The
patient presented with failure to thrive, exercise
intolerance during daily activities, and a history of
recurrent respiratory tract infections. Echocardiography
and right heart catheterization (RHC) results showed that
the first patient with VSD Left to Right Shunt with low
flow high resistance, non-reactive oxygen test and
pulmonary hypertension. The second patient with VSD
Let to Right shunt. Both of the patients were diagnosed
with ventricular septal defect (VSD) and pulmonary
hypertension (PH). However, they received different
treatments based on the RHC results.
Conclusion:
Promptly addressing the long-term implications of
CHD is essential to prevent pulmonary hypertension (PH)
and systemic disorders. Advanced PH treatments are safe
and can result in improved hemodynamic, exercise
capacity, quality of life, growth and development and
potentially survival.
Keywords :
Congenital Heart Disease, Ventricle Septal Disease, Twins, Pulmonary Arterial Hypertension, Right Heart Catheterization.
