Rhabdomyosarcoma is an extremely aggressive malignant tumor that rarely occurs in adults. Its orbital location represents only 9% of all head and neck injuries. We report the clinical case of an orbital rhabdomyosarcoma in adults. Observation: This is a 23 year old adult; of Moroccan nationality, which had presented a right exophthalmia of progressive evolution with cervical lymphadenopathy. The clinical examination had objectified a right exophthalmia and upper internal jugular lymphadenopathy; the rest of the clinical examination was without particularity. Computed tomography revealed a right intra-orbital tumor process. Histological analysis revealed an embryonic rhabdomyosarcoma with lymph node metastases. The combination of ifosfamide, vincristine and actinomycin chemotherapy and 66 Gy orbital radiation therapy using the intensity modulation technique (IMRT) resulted in complete remission with a 6-month setback. Conclusion: Rhabdomyosarcoma is a rare tumor. Early management improves the prognosis of life and function

Keywords : Rhabdomyosarcoma, Orbital Tumor, Radiotherapy, Chemotherapy