Authors : Hassnaa Sarhane; Kaoutar Bahida; Maha Lhaloui; Nouhaila Yartaoui; Riache Hafsa; Najia Zeraidi; Amina Etber; Aziz Baydada

Volume/Issue : Volume 10 - 2025, Issue 7 - July

Google Scholar : https://tinyurl.com/3s53m3pj

Scribd : https://tinyurl.com/5b546wsc

DOI : https://doi.org/10.38124/ijisrt/25jul1419

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Abstract : Potter syndrome, also known as Potter sequence, is a rare and lethal congenital condition caused by bilateral renal agenesis, which leads to severe oligohydramnios, pulmonary hypoplasia, and characteristic facial and limb deformities. We present the case of a 40-year-old gravida 4 para 3 woman referred for evaluation of anhydramnios at 27 weeks gestation. Ultrasound revealed absent fetal kidneys, an empty bladder, and severe oligohydramnios, signs consistent with a diagnosis of Potter syndrome. The fetus didn’t show features suggestive of Potter facies or limb deformities. The pregnancy was continued after counseling. The neonate died shortly after birth due to respiratory failure. Potter syndrome carries a uniformly poor prognosis. Prenatal diagnosis is essential for guiding clinical decisions, psychological support, and ethical counseling. A multidisciplinary approach is crucial in managing affected pregnancies and supporting families.

Keywords : Potter Syndrome, Potter Sequence, Bilateral Renal Agenesis, Pulmonary Hypoplasia, Oligohydramnios, Prenatal Diagnosis, Fetal Anomalies.

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