Authors :
Dr. Harsh Aggarwal; Dr. Vibhor Garg; Dr. Sonika Lamba; Dr. Shubham Gupta; Dr. Aneeshya CK
Volume/Issue :
Volume 8 - 2023, Issue 4 - April
Google Scholar :
https://bit.ly/3TmGbDi
Scribd :
https://bit.ly/415psH5
DOI :
https://doi.org/10.5281/zenodo.7894400
Abstract :
Undifferentiated pleomorphic sarcoma
(UPS) was earlier termed as malignant fibrous
histiocytoma (MFH). UPH mainly affects extremities
and retroperitoneum with the age predisposition of 50+.
We present a case of 16 year old boy with malignant
UPS; primary in thigh with lung metastases showing an
excellent response to multidisciplinary approach
involving surgeryfollowed by systemic combination
chemotherapy. The treatment of the patient with
metastatic UPS/MFH was successfulutilizing a
multidisciplinary approach; although, this type of
sarcoma carries a poor prognosis and seen to be
insensitive to both chemotherapy and radiotherapy.
Keywords :
Undifferentiated pleomorphic sarcoma, Malignant fibrous histiocytoma, Chemo radiotherapy.
Undifferentiated pleomorphic sarcoma
(UPS) was earlier termed as malignant fibrous
histiocytoma (MFH). UPH mainly affects extremities
and retroperitoneum with the age predisposition of 50+.
We present a case of 16 year old boy with malignant
UPS; primary in thigh with lung metastases showing an
excellent response to multidisciplinary approach
involving surgeryfollowed by systemic combination
chemotherapy. The treatment of the patient with
metastatic UPS/MFH was successfulutilizing a
multidisciplinary approach; although, this type of
sarcoma carries a poor prognosis and seen to be
insensitive to both chemotherapy and radiotherapy.
Keywords :
Undifferentiated pleomorphic sarcoma, Malignant fibrous histiocytoma, Chemo radiotherapy.