Authors : Dr. Aswin Sasikumar; Dr. V. A. Kothiwale

Volume/Issue : Volume 10 - 2025, Issue 2 - February

Google Scholar : https://tinyurl.com/3ys73h2x

Scribd : https://tinyurl.com/fxz3sk72

DOI : https://doi.org/10.5281/zenodo.14928744

Abstract : A 45-year-old male presented with status epilepticus and was subsequently diagnosed with Dyke-Davidoff-Masson Syndrome (DDMS), a rare neurological disorder characterized by cerebral hemiatrophy, seizures, hemiplegia, and cranial asymmetry. This case highlights the clinical features, imaging findings, and management of DDMS in adulthood, contributing to the limited literature on late presentations of this syndrome. The patient's acute condition was managed with antiepileptic therapy, and follow-up strategies were established to address chronic neurological deficits. This report underscores the need for heightened awareness of DDMS in adult seizure presentations and provides insights into its long- term management.

Keywords : Dyke-Davidoff-Masson Syndrome, Status Epilepticus, Cerebral Hemi atrophy, Seizures, Hemiplegia.

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