Authors : Dr. Saurav Shankar Das; Dr. Nandini N. Krishnamurthy; Dr. Grace Mary Joseph; Dr. Shijal Narayan; Dr. Riolla Sanchia Dsouza

Volume/Issue : Volume 9 - 2024, Issue 6 - June

Google Scholar : https://tinyurl.com/4a6tp4by

Scribd : https://tinyurl.com/6ryse5mu

DOI : https://doi.org/10.38124/ijisrt/IJISRT24JUN1954

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Abstract : Darier disease (DD), also known as keratosis folicularis and White disease , is an inherited autosomal dominant genodermatosis. DD often develops in childhood, persists through adolescence and causes small papules predominantly in seborrheic areas such as the face , chest and back. The oral lesions are asymptomatic and comprise multiple white papules in the buccal mucosa and the soft and hard palate , giving a cobblestone appearance. Histologically , DD is characterized by corps ronds and grains in addition to suprabasal cleavage. There are no currently validated curative treatments available for DD, with the majority of cases treated symptomatically. This is a case report of DD with varied manifestations intraorally and extraorally. Diagnosis was established on the basis of clinical , histopathological and dermatological findings. Patient reported to the OPD with a chief complaint of loose teeth. A holistic treatment approach was carried out based on clinical and histological findings. Functional and esthetic demands were met with satisfactory results.

Keywords : Dariers Disease , Extraction , Complete Denture ,Biopsy.

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