Follicular dendritic cell sarcoma is a rare location and are generally indolent. whose diagnosis is essentially anatomopathological which remains delicate in view of the similarity with other types of soft tissue sarcomas, the therapeutic strategy is not clear because of the rarity of cases reported by the literature. We describe the case of a 30-year-old patient followed for tonsil mass, pathologic study revealed of a dendritic follicular cell sarcoma of the tonsillar epithelioid type, the systemic treatment for his metastatic relapse. In this article on will raise the clinical, histology and therapeutic aspects of this location with a review of literature.

Keywords : Tonsillar, Follicular Dendritic Cell Sarcoma, Metastasis, Chemotherapy