Authors : Dr. Shivansh Yadav; Dr. Jayprakash A; Dr. Rekha S Patil

Volume/Issue : Volume 10 - 2025, Issue 2 - February

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Google Scholar : https://tinyurl.com/vkych82w

Scribd : https://tinyurl.com/2kjc2dp2

DOI : https://doi.org/10.38124/ijisrt/25feb1488

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Abstract : Hemophagocytic lymphohistiocytosis (HLH) is a rare but potentially fatal hyperinflammatory syndrome characterized by excessive immune activation. The condition may be genetic (primary HLH) or secondary to infections, malignancies, or autoimmune diseases. Early diagnosis and prompt treatment are essential to prevent multi-organ failure and mortality. We present a case of HLH diagnosed based on clinical and laboratory criteria, highlighting the diagnostic challenges, treatment approach, and patient outcome.

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