Congenital factor V deficiency (CFVD) is a
rare coagulation disorder, also known as para
hemophilia, that was first described by Owren in 1947.
Until now, no specific protocols for the management of
these patients have been established, owing to the variable
spectrum of bleeding manifestations. However, available
research suggests that perioperative infusion of fresh
frozen plasma (FFP) may aid in maintaining FV levels to
prevent bleeding. We present the case of a 47-year-old
woman with congenital FV deficiency who underwent
cochlear implantation with no postoperative hemorrhagic
Factor V, Congenital Factor V Deficiency, Perioperative Management, Cochlear Implantation, Hemostasis, Hematology, Case Report.